DAILY PROGRAM


April 2, Wednesday
Time No. Program
8:15-8:30 OPENING

OPENING ADDRESS I. II., and III.
Mitarai, G. / Nagoya , Japan
Miyake, Y. / ISCEV President
8:30-9:00 INVITED MAIN LECTURE I.
Chairs: Niemeyer, G. & Oguchi, Y.

RESPONSE OF GENETICALLY-DAMAGED PHOTORECEPTORS TO ADENO-ASSOCIATED VIRUS-MEDIATED CILIARY NEUROTROPHIC FACTOR THERAPY AND TO AN INDUCIBLE RESCUE GENE IN AN ANIMAL MODEL: MORPHOLOGICAL AND ELECTRORETINOGRAPHIC (ERG) CHANGES
Bok, D.
Jules Stein Eye Institute, University of California, Los Angeles, California, USA
ORAL SESSION I.
Night Blinding Disorders: Animal Model and Clinical Investigations I.
Chairs: Niemeyer, G. & Oguchi, Y.
9:00-9:15 O1 COMPLETE TYPE OF CONGENITAL STATIONARY NIGHT BLINDNESS:
PUZZLING MACULAR FUNCTION

Kondo, M., Ueno, S., Niwa, Y., Asano, T., Suzuki, S., Terasaki, H. and Miyake, Y.
9:15-9:30 O2 X-LINKED CONGENITAL STATIONARY NIGHT BLINDNESS:
MUTATIONS IN CACNA1F AND THE CONSTRUCTION OF A MOUSE MODEL OF iCSNB

Bech-Hansen, N., Mansergh, F., Tremblay, F., Lalonde, M., Vessey, J., Barnes, S., Weleber, R., Robitaille, J., Boycott, K., Rancourt, D. and CSNB Consortium
9:30-9:45 O3 SLOW AND FAST ROD PATHWAYS IN CSNB1, CSNB2 AND AUTOSOMAL RECESSIVE CONGENITAL STATIONARY NIGHT BLINDNESS
Van Genderen, M. and Riemslag, F.
9:45-10:00 O4 FOUR-YEAR OUTCOMES FROM A RANDOMIZED CINICAL TRIAL OF DOCOSAHEXAENOIC ACID (DHA) SUPPLEMENTATION IN X-LINKED RETINITIS PIGMENTOSA (XLRP)
Birch, D., Wheaton, D., Locke, K., Fish, G. and Hoffman, D.

10:00-11:00
POSTER SESSION I.
ERG: Clinical Studies
Chair: Yamamoto, S.
P1 THERE IS A NORMAL PHOTOPIC ELECTRORETINOGRAM LIGHT RISE IN RETINITIS PIGMENTOSA
Vaegan, Lowry, B. and Beaumont, P.
P2 X-LINKED JUVENILE RETINOSCHISIS DIAGNOSED BY THE DNA ANALYSIS PRIOR TO THE ELECTROPHYSIOLOGICAL EXMINATION
Hotta, Y., Kawano, T., Nishimura, K., Kato, M. and Sato, M.
P3 AGE OF ONSET OF ERG CHANGES IN USHER'S SYNDROME
Thompson, D., Russell-Eggitt, I. and Bitner-Glindtziz, M.
P4 BRIGHT FLASH ERG TO INVESTIGATE ROD SYSTEM DYSFUNCTION
Westall, C. and Wright, T.
P5 ELECTROPHYSIOLOGICAL FINDINGS IN X-LINKED RP PATIENTS WITH MUTATIONS OF RPGR GENE
Nao-i, N., Uchida, A., Liu, X., Jin, Z., Yokoyama, A., Hayakawa, M. and Murakami, A.
P6 EFFECT OF LONG-TERM LIGHT EXPOSURE ON RETINAL FUNCTION OF OUTDOOR AND INDOOR WORKERS
Rufiange, M., Dumont, M. and Lachapelle, P.
P7 SOLAR RETINOPATHY IN A SCHIZOPHRENIA PATIENT WITH ABNORMAL ELECTRORETINOGRAM
Murayama, K., Ito, M., Saito, S., Nishikawa, M. and Yoneya, S.
P8 NONARTERITIC ANTERIOR ISCHEMIC OPTIC NEUROPATHY IN DIABETIC PATIENTS. AN ELECTROPHYSIOLOGICAL STUDY
Janaky, M., Fulop, Zs, Palffy, A. and Benedek, G.
P9 THE EFFECT OF TILT TABLE TEST ON ERGS IN PATIENTS WITH PRIMARY OPEN ANGLE GLAUCOMA
Kolotov, A. and Astakhov, Yu
P10 OCULAR ELECTROPHYSIOLOGY FOR EVALUATION OF CASES WITH UNEXPLAINED VISION LOSS
Al-Nahrawy, O.
P11 FOVEAL THICKNESS IN OCCULT MACULAR DYSTROPHY
Ueno, S., Kondo, M., Ito, Y., Piao, CH., Terasaki, H. and Miyake, Y.
P12 CHANGE IN FOCAL MACULAR ERGS AFTER MACULAR TRANSLOCATION SURGERY WITH 360-DEGREE RETINOTOMY
Terasaki, H., Niwa, Y., Ishikawa, K., Piao, CH., Niwa, T., Ito, Y., Suzuki, S., Kondo, M., and Miyake, Y.
P13 PHOTORECEPTOR SPECIFIC ADAPTATION IN S-CONE MONOCHROMAT
Stepien, M., Zrenner, E. and Kremers, J.
P14 WHAT DO ISCEV STANDARD PHOTOPIC ERGS REPRESENT IN A BLUE-CONE MONOCHROMAT ?
Rigaudiere, F., Rosolen, S., Bitoun, P., Lachapelle, P. and LeGargasson, J-F.
P15 TWO CASES OF SPINOCEREBELLAR DEGENERATION WITH NEGATIVE ELECTRORETINOGRAMS
Yamazaki , H., Taniai , A., Kimura , A., Nemoto , H. and Yuasa, T.
P16 NIGHT BLINDNESS WITH ATYPICAL DEPOLARIZING PATTERN OF ON-OFF RESPONSE: A CASE REPORT
Usui, T., Tanimoto, N., Takagi, M., Hasegawa, S., and Abe, H.
P17 DISORDERS OF THE RETINAL PIGMENT EPITHELIUM IN A PATIENT WITH AQUIRED OCULAR TOXOPLASMOSIS
Kato, C., Asakura, A., Chen, R., Kubo, S., and Mori, T.
P18 ABNORMAL ELECTROMYOGRAPHIC FINDINGS IN A PATIENT WITH NEGATIVE SCOTOPIC ELECTRORETINOGRAM AND NORMAL DARK ADAPTATION
Tanimoto, N., Usui, T., Takagi, M., Hasegawa, S., Abe, H. and Tanaka, K.
11:00-11:20 INVITED INTRODUCTORY LECTURE I.
Chairs: Brigell, M. & Vaegan

TOWARDS A LAYER- AND LOCATION-SPECIFIC ASSESSMENT OF FUNCTION IN ANIMAL MODELS OF INHERITED RETINAL DEGENERATIONS
Seeliger, M. / Retinal Electrodiagnostics Research Group, Dept. of Ophthalmology II, University of Tuebingen, Germany
ORAL SESSION II.
Night Blinding Disorders: Animal Model and Clinical Investigations II.
Chairs: Brigell, M. & Vaegan
11:20-11:35 O5 COMPARISON OF PAIRED-FLASH ERG-DERIVED ROD PHOTORESPONSES DETERMINED IN NORMAL AND nob (NO b-WAVE) MICE
Kang Derwent, J., Saszik, S., Pardue, M., Frishman, L. and Pepperberg, D.
11:35-11:50 O6 CONSIDERATION OF ENDOGENOUS FREE ZINC AS A FACTOR IN NIGHT BLINDNESS: IMPLICATIONS FROM THE SKATE ERG
Chappell, R. and Redenti, S.
11:50-12:05 O7 CONGENITAL STATIONARY NIGHT BLINDNESS (CSNB) RESULTING FROM A LACK OF RODS: THE GUINEA PIG MODEL
Racine, J., Moukhles, H. and Lachapelle, P.
12:05-12:20 O8 BILATERAL LONG-TERM ELECTRORETINOGRAPHIC EFFECTS AND VISUAL BEHAVIOR CORRELATES FOLLOWING UNILATERAL RAAV.RPE65 GENE TRANSFER IN RPE65-/- DOGS
Bragadottir, R., Ford, M. and Narfstrom, K.
12:40-13:40

LUNCHEON SEMINAR - PDE Type-5 Inhibitor and Eyesponsored by Pfizer

THE EFFECT OF SILDENAFIL ON VISUAL FUNCTION - CHAIRMAN'S INTRODUCTION
Harding, G. / Neurosciences Institute, Aston University, Birmingham, UK

ACUTE EFFECTS OF SILDENAFIL ON THE ELECTRORETINOGRAM
Marmor, M. / Department of Ophthalmology, Stanford University Medical Center, Stanford, California, USA

THE EFFECTS OF SILDENAFIL CITRATE ON VISION IN PATIENTS WITH AGE-RELATED MACULAR DEGENERATION (ARMD)
Birch, D. / Retina Foundation of the Southwest,Department of Ophthalmology, UT Southwestern, Dallas, Texas, USA

MATHEMATICAL RETINAL MODEL PROVIDES THE WAY TO TEST SIDE EFFECT OF SILDENAFIL
Usui, S. / Toyohashi University of Technology, Toyohashi, Japan

14:00-14:20 INVITED INTRODUCTORY LECTURE II.
Chairs: Horiguchi, M. & Marmor, M.

PARANEOPLASTIC AND AUTOIMMUNE RETINOPATHY
Weleber, R. / Casey Eye Institute, Oregon Health & Science University, Portland, Oregon, U.S.A.
ORAL SESSION III.
ERG:Clinical Applications
Chairs: Horiguchi, M. & Marmor, M.
14:20-14:35 O9 ELECTRORETINOGRAPHIC AND OPHTHALMIC FINDINGS OF CRMP-5 AUTOANTIBODY PARANEOPLASTIC SYNDROME
Lam, B., Cross, S. and Lennon, V.
14:35-14:50 O10 PHENOTYPIC VARIATIONS IN ENHANCED S-CONE SYNDROME (ESCS)
Holder, G., Hogg, C., Neveu, M., Robson, A. and Bird, A.
14:50-15:05 O11 THE CIRCADIAN CHANGES IN L- AND M-CONE ISOLATING ERG SIGNALS AND EFFECT OF CONE SELECTIVE ADAPTATION
Stepien, M., Czop, D., Zrenner, E. and Kremers, J.
15:05-15:35 COFFEE BREAK
15:35-15:55 INVITED INTRODUCTORY LECTURE III.
Chairs: Bach, M. & Mizota, A.

VEP STUDY FOR LEBER'S OPTIC NEUROPATHY AND OPTIC NEURITIS
Oguchi, Y. / Department of Ophthalmology, School of Medicine, Keio University, Tokyo
15:55-16:15 INVITED INTRODUCTORY LECTURE IV.
Chairs: Bach, M. & Mizota, A.

UNLEASHING THE VISUALLY EVOKED POTENTIAL
Barber, C. / Queen's Medical Centre, Nottingham, UK
ORAL SESSION IV.
VEP
Chairs: Bach, M. & Mizota, A.
16:15-16:30 O12 DIAGNOSTIC PROFIT FROM SEPARATE MACULAR AND PERIPHERAL STIMULATION IN PATTERN AND MOTION RELATED VEPS
Kuba, M., Chlubnova, J., Kremlacek, J., Szanyi, J., Kubova, Z. and Vit, F.
16:30-16:45 O13 IMPROVED SUCCESS IN PAEDIATRIC ACUITY ASSESSMENT
Mackay, A., Bradnam, M., Hamilton, R., Dutton, G. and Spowart, K.
16:45-17:00 O14 ASSESSING CONTRAST SENSITIVITY AND VISUAL ACUITY USING SWEEP VISUAL EVOKED POTENTIALS IN INFANTS TAKING VIGABATRIN
Morong, S., Westall, C., Buncic, J., Snead, O., Logan, W. and Weiss, S.

17:00-18:00
POSTER SESSION II.
VEP
Chair: Kuba, M.
P19 FIELD SPECIFIC VEP ASSESSMENT OF POSSIBLE FIELD DEFECTS IN CHILDREN ON VIGABATRIN-TREATED MOTHERS AND ADULTS WITH LEARNING DIFFICULTIES
Harding, G. and Spencer, E.
P20 RAPID RECORDING OF SPATIAL FREQUENCY SWEEP PATTERN VISUAL EVOKED CORTICAL POTENTIALS USING A LOCK-IN AMPLIFIER
Sato, E., Uemura, A., Mizota, A., and Adachi-Usami, E.
P21 SUBJECT-SPECIFIC MACULAR PIGMENTATION INFLUENCES THE SELECTIVITY OF CHROMATIC VEPS
Robson, A., Holder, G., Fitzke, F., Moreland, J. and Kulikowski, J.
P22 "ADAPTIVE VEPs" MAY IMPROVE THE OBJECTIVE ESTIMATION OF SENSORY THRESHOLDS. AN APPLICATION OF PSYCHOPHYSICAL PROCEDURES TO STEADY-STATE CONTRAST VEP RECORDINGS
Meigen, T. and Kley, F.
P23 P100 LATENCY DEPENDENCY ON THE MODE OF OPERATION OF THE PATTERN GENERATOR
Brown, M. and Hagan, R.
P24 ENHANCEMENT OF MACULAR FIELD DEFECTS ON REVERSING CHECKERBOARD SCREENS
Brown, M. and Hagan, R.
P25 QUADRANTIC CHECKERBOARD PATTERN REVERSAL VEFS: EFFECT OF THE CHECK-SIZE
Takimoto, M., Yanashima, K. and Magatani K.
P26 BINOCULAR SUMMATION OF PVECPS IN PATIENTS WITH UNILATERAL OPTIC NEURITIS
Mizota, A., Hoshino, A., Sato, E., Tsuyama, Y., and Adachi-Usami, E.
P27 VEPS IN CONGENITAL NYCTALOPIA
Kubova, Z., Kremlacek, J., Kuba, M., Chlubnova, J. and Szanyi, J.
P28 HOW TO TEST PARVOCELLULAR PATHWAY IN CHILDREN?
TekavčDič-Pompe, M., Brecelj. J., and Stirn-Kranjc, B.
P29 PEDIATRIC ELECTROPHYSIOLOGY UNDER GENERAL ANESTHESIA
Shehab, A.
P30 FLASH VECPs IN A CHILD WITH CORTICAL BLINDNESS FOLLOWING OPEN-HEART SURGERY
Asaumi, N., Mizota, A., and Adachi-Usami, E.
P31 TRANSIENT VEPS IN CHILDREN WITH DOWN SYNDROME
Suttle, C. and Turner, A.
P32 ELECTROPHYSIOLOGICAL CORRELATES OF TRAUMATIC BRAIN INJUY SEVERITY
Lachapelle, J., Thibault, G. and McKerral, M.
P33 OPTIMALISATION OF RADIAL MOTION STIMULI FOR VEPS EXAMINATION
Kremlacek, J., Chlubnova, J. and Kuba, M.
P34 CHARACTERISTICS OF FIRST AND SECOND ORDER KERNELS OF VISUALLY EVOKED POTENTIALS ELICITED BY PSEUDORANDOM STIMULATION
Nemoto, N., Momose, K., Kiyosaw, M., Mori, H. and Mochizuki, M.
P35 RELATIONSHIP BETWEEN VISUAL FIELD DEFECT AND MULTIFOCAL VISUAL EVOKED POTENTIAL
Takahashi, Y., Satoh, N., Tazawa, Y. and Kamei, A.
P36 SIMULTANEOUOS RECORDINGS OF THE MULTIFOCAL ERGs AND MULTIFOCAL VEPs IN PATIENTS WITH VARIOUS OPHTHALMIC DISORDERS
Hasegawa, S., Usui, T., Tanimoto, N., Ikeda, J., Miki, A., Takagi, M., and Abe, H.
P37 MULTIFOCAL VISUAL EVOKED MAGNETIC RESPONSES TO DARTBOARD PATTERN REVERSAL STIMULATION
Wen, Y., Barber, C., Wang, L. and Kakigi, R.
P38 MAGNETOENCEPHALOGRAPHIC (MEG) STUDIES OF BINOCULAR FUSION, RIVALRY AND STEREOSIS IN HUMANS
Shahani, U., McCulloch, D. and Simpson, W.
P39 CORTICAL MORPHOLOGIC CHANGES CHARACTERIZE ANISOMETROPIC AND STRABISMIC AMBLYOPIA
Odom, J., Mendola, J., Roy, A., Conner, I., Chan, ST., Kwong, K. and Fischl, B.
18:30-19:30 KYOGEN NIGHT - performed by the Shigeyma "BOH-SHIBARI"
19:30-21:30 DINNER (KKR Hotel, Room Fuyo & Ran)



top of this page